Response to “Chromosomal Abnormalities and Neuromuscular Disorders Predict Severity and Outcome of Noncompaction in Addition to Cardiac Comorbidities”

Apical short-axis dissection of a pathologic specimen in a patient who died in our series from left ventricular noncompaction and Ebstein's anomaly. The noncompaction (NC) is noted at the apex of the left ventricle (LV). The tricuspid valve (TV) apparatus is significantly displaced into the apical region, while the right ventricle (RV) demonstrates significant dilation and hypertrophy. The length of the black line represents 1 cm. This image was obtained courtesy of Andrew J. Connolly, MD, PhD, Stanford University, Lucille Packard Children's Hospital. ∗Middle cardiac vein.